Management of Ebstein's anomaly.
نویسندگان
چکیده
Ebstein malformation is a rare disease that presents with a spectrum of severity. We use a management paradigm that breaks the anomaly into two groups: neonates and children/adults. This leads to a discussion of management and operative techniques as well as pitfalls. We hope the reader finds our streamlined and logical approach of benefit to this complex and rare disease.
منابع مشابه
Ebstein's anomaly of the tricuspid valve.
Ebstein's anomaly of the tricuspid valve is a rare lesion comprising less than 1% of patients with congenital heart disease. Among congenital heart lesions, Ebstein's anomaly is one of the most diverse in presentation, severity, and management. In its most severe form, it is also one of the most lethal. In this article we present a case of a patient who developed cardiac symptoms in adulthood. ...
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Background. Ebstein's anomaly is the most commonly occurring congenital abnormality associated with the Wolif-Parkinson-White (WPW) syndrome. However, the effects of Ebstein's anomaly on the risks and benefits of surgical ablation of accessory pathways in patients with WPW syndrome are unknown. Methods and Results. This study compared the long-term outcome of 38 WPW patients with Ebstein's anom...
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The coexistence of rheumatic mitral stenosis, Ebstein's anomaly and Wolff-Parkinson-White syndrome is an uncommon entity. To our knowledge, the successful management of this combination of lesions has not been previously described. We report a 23-year-old woman with the combination of these abnormalities. She was managed with preoperative electrophysiological study, followed by mitral valve rep...
متن کاملManagement and outcome of Ebstein's anomaly in children.
OBJECTIVES To assess clinical presentation, treatment, and outcome of children with Ebstein's anomaly. BACKGROUND Data on long-term outcome of children with Ebstein's anomaly are scarce. METHODS Retrospective analysis of all children with Ebstein's anomaly treated between February, 1979 and January, 2009 in a single tertiary institution. Primary outcomes included patient survival and need f...
متن کاملAtrialised right ventricular myxoma in a patient with Ebstein’s anomaly
Ebstein's anomaly is a rare entity affecting around 1 in 200,000 live births and accounts for less than 1% of congenital heart diseases. Ebstein's anomaly with an associated right-sided myxoma is extremely rare, with only one other case report found in the literature. Previous reports have also noted cases of Ebstein's anomaly associated with left-sided myxomas. We describe a female patient wit...
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INTRODUCTION AND OBJECTIVES The development of ablation techniques for supraventricular arrhythmias in patients with Ebstein's anomaly have led to a need for better understanding of the morphology of the triangle of Koch and the position of the atrioventricular (AV) node in this structure. METHODS The study involved 17 human hearts: 11 with Ebstein's anomaly (age range: 37 weeks' gestation to...
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ورودعنوان ژورنال:
- Annals of cardiothoracic surgery
دوره 6 3 شماره
صفحات -
تاریخ انتشار 2017